Menene alamun hemochromatosis?

Menene alamun hemochromatosis?

Alamu suna da alaƙa da adon baƙin ƙarfe akan gabobin jiki daban -daban kamar fata, zuciya, glandon endocrine da hanta.

Juyin halitta na alamun cututtuka

- Tsakanin shekaru 0 zuwa 20, ƙarfe a hankali yana tarawa cikin jiki ba tare da haifar da alamu ba.

- Tsakanin shekaru 20 zuwa 40, wucewar baƙin ƙarfe yana bayyana wanda har yanzu bai ba da alamun cutar ba.

- A tsakiyar tsakiyar shekaru goma na huɗu a cikin maza (kuma daga baya a cikin mata), alamun asibiti na farko na cutar sun bayyana: gajiya Dindindin hadin gwiwa zafi (ƙananan haɗin yatsun hannu, wuyan hannu ko kwatangwalo), launin fata (melanoderma), bayyanar “launin toka, ƙarfe” fatar fuska a fuska, manyan gidajen abinci da al'aura, atrophy na fata (fatar ta zama sirara), ɓarna ko sikelin sikelin kifi (wannan shine abin da ake kira ichthyosis) na fata da raunin gashi da gashin gindi

- Lokacin da ba a gano ganewar cutar ba, matsalolin suna bayyana suna shafar hanta, zuciya da kuma endocrine gland.

Cinwan lalata : akan gwajin asibiti, likita na iya lura da karuwar girman hanta, da alhakin ciwon ciki. Cirrhosis da fara ciwon sankarar hanta su ne mafi girman matsalolin cutar.

Haɗuwa da tsarin endocrine : za a iya nuna alamar cutar ta aukuwar ciwon suga (lalacewar farji) da rashin ƙarfi a cikin maza (lalacewar gwaiwa).

Lalacewar zuciya : Ajiye baƙin ƙarfe akan zuciya shine ke da alhakin ƙaruwarsa da alamun gazawar zuciya.

Don haka, idan cutar ta kamu da cutar ne kawai a ƙarshen mataki (lamuran da suka rage na yau), yana yiwuwa a lura da haɗarin bugun zuciya, ciwon sukari da cirrhosis na hanta. da launin launin ruwan kasa na fata.

 

Da farko an gano cutar (kafin shekarun 40), mafi kyawun martani ga jiyya da kyakkyawar hasashen cutar.. A gefe guda, lokacin da rikitattun abubuwan da aka bayyana a sama suka bayyana, suna komawa baya a ƙarƙashin magani. Idan an yi wa mai haƙuri magani kafin fara cirrhosis, tsawon rayuwarsu daidai yake da na yawan jama'a.

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