Jiyya, gudanarwa, rigakafin hemochromatosis

Jiyya, gudanarwa, rigakafin hemochromatosis

Jiyya na hemochromatosis ya dogara ne akan zubar jini (wanda kuma ake kira phlebotomies). Suna da niyyar rage matakin ƙarfe a cikin jini da rage adadin baƙin ƙarfe a cikin jiki ba tare da haifar da raunin baƙin ƙarfe ba.

Hanyar tana daidai da wacce aka yi yayin bayar da jini. Ana so a sha ruwa bayan zubar jini.

Magani ne mai sauƙi, mai arha kuma mai inganci, yawanci ana yin shi tsakanin sau 4 zuwa 6 a shekara, ba tare da tasiri ga rayuwar mai haƙuri ba, musamman tunda ana iya yin jinin a gida.

Likitan ya bayyana adadin jinin da za a ɗauka ya bayyana a kai a kai a cikin mai haƙuri la'akari da shekarunsa, nauyi da tsayinsa. Da farko, zubar jini na mako -mako ya zama dole kuma ana kiyaye shi muddin ana lura da yawan ƙarfe. Lokacin da matakin ferritin a cikin jini ya faɗi ƙasa da 50 μg / L, ana yin su kowane wata ko kwata kamar yadda lamarin zai iya kasancewa don kula da matakin ferritin a cikin jinin da ke ƙasa 50 μg / L. Za a kiyaye su har tsawon rayuwa.

Wannan magani baya warkar da cutar.

A cikin mata masu juna biyu, ba a yin zubar da jini a duk lokacin ciki. Ƙarin ƙarfe ba lallai ba ne.

Sauran matsalolin cutar (cirrhosis, gazawar zuciya ko ciwon sukari) sune batun takamaiman magani.


Lura cewa babu wani abincin da zai maye gurbin magani ta zubar da jini. Ana ba da shawarar mai haƙuri ya bi tsarin abinci na yau da kullun da iyakance shan barasa.

 

Amfanin magani

Tare da magani, gajiya da ake gani a cikin marasa lafiya da hemochromatosis ya ragu. Musamman, lokacin da aka fara magani da wuri, yana taimakawa don guje wa mummunan rikitarwa na cutar (lalacewar zuciya, hanta da pancreas) don haka yana ƙara tsawon rayuwar marasa lafiya.

Babu wani canji a cikin halaye na marasa lafiya da za a yi la’akari da shi a cikin hemochromatosis ban da ƙa'idodin tsabtace rayuwa wanda ya haɗa da abinci na yau da kullun da rage abubuwan sha idan an yi wuce gona da iri.

Ana kula da marasa lafiya a cikin sassan hepato-gastroenterology. A cikin mutanen da ke cikin haɗari, ana nuna cikakkiyar shawarwarin kwayoyin halitta don gano cutar da wuri kuma ɗaukar matakan warkarwa da suka dace.

A cikin Faransa, nau'ikan hemochromatosis na ci gaba suna ɗaya daga cikin yanayin 30 na dogon lokaci (ALD 30).

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